Wiskott-Aldrich Syndrome

Medical Dictionary -> Wiskott-Aldrich Syndrome

Wiskott-Aldrich Syndrome


A rare, X-linked immunodeficiency syndrome characterized by eczema, thrombocytopenic purpura, and recurrent pyogenic infection. It is seen exclusively in young boys. Typically, IMMUNOGLOBULIN M levels are low and IMMUNOGLOBULIN A and IMMUNOGLOBULIN E levels are elevated. Lymphoreticular malignancies are common.


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